INHERITED METABOLIC DISEASES (IMD), SUCH AS ORGANIC ACIDEMIAS (OAS) AND FATTY ACID OXIDATION DEFECTS (FAODS) HAVE BECOME TO ATTRACT ATTENTION WITH THE DEVELOPMENT OF DIAGNOSTIC TOOLS INCLUDING TANDEM MASS SPECTROMETRY (MS/MS), AND GAS CHROMATOGRAPHY MASS SPECTROMETRY (GC/MS). PATIENTS WITH OAS OR FAODS OFTEN MANIFEST EPISODIC FATIGUE, HYPOTONIA, CONVULSION, OR ACUTE ENCEPHALOPATHY FOLLOWING PYREXIA, DIARRHEA OR LONG TIME FASTING, ALTHOUGH NO SYMPTOMS ARE OBSERVED IN THE STABLE STAGE...